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KMID : 1144020190150010029
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Journal of Korean Association for Disability and Oral Health
2019 Volume.15 No. 1 p.29 ~ p.34
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DENTAL MANAGEMENT OF A 46-MONTH-OLD CHILD WITH PRADER-WILLI SYNDROME : A CASE REPORT
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Choi Kyung-Hwa
Kim Mi-Sun
Nam Ok-Hyung
Lee Hyo-Seol
Choi Sung-Chul
Kim Kwang-Chul
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Abstract
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Prader-Willi Syndrome (PWS) is a rare neurologic disorder with a prevalence 1/10,000-30,000. The cause of PWS is an abnormalities of chromosome 15q11.2-q13 which is an imprinting gene. Obesity and hyperphagia are characteristic features on a PWS adult. On the other hand, the birth weight, height and body mass index (BMI) of PWS infants are 15-20% lower than those of normal babies and there is a failure to thrive until 24-month-old. Most of PWS patients are treated under general anesthesia and conscious sedation. This case is a treatment of severe caries in a PWS 46 month-old child without general anesthesia and conscious sedation. He came to the Department of Pediatric Dentistry, Kyung Hee University Dental Hospital at Gangdong, Seoul, Korea with a trauma history. He had a medical history with heart surgery and needed to take antibiotics prophylaxis. The luxated left upper primary tooth were removed and caries treatment were done as an outpatient without general anesthesia, conscious sedation.
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KEYWORD
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Prader-Willi Syndrome, Outpatient treatment of PWS, Trauma of PWS
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